The Hallermann Strieff syndrome (HSS) is a rare congenital disorder characterized by distinctive craniofacial malformations and significant orodental abnormalities. Very few such cases have been reported in the literature. Most cases of hallermann–strieff syndrome occur randomly, for unknown reason, may be the result of mutations, or changes in the genetic material. HSS is associated not only with developmental anomalies involving structures of ectodermal origin (face, skull, hair, skin, eyes and teeth) but also affects overall growth and development. One of such rare case of hallermann streiff syndrome reported at Department of Orthodontics, Government Dental College and Hospital, Ahmedabad with chief complaint of proclination of maxillary anterior is presented.
